Kim G. Nielsen

Kim G. Nielsen

Clinical Professor

Member of:

  • Paediatrics


  1. 2024
  2. Published

    A BEAT-PCD consensus statement: a core outcome set for pulmonary disease interventions in primary ciliary dyskinesia

    Kos, R., Goutaki, M., Kobbernage, H. E., Rubbo, B., Shoemark, A., Aliberti, S., Altenburg, J., Anagnostopoulou, P., Athanazio, R. A., Beydon, N., Dell, S. D., Emiralioglu, N., Ferkol, T. W., Loebinger, M. R., Lorent, N., Maître, B., Marthin, J., Morgan, L. C., Nielsen, K. G., Ringshausen, F. C. & 6 others, Shteinberg, M., Tiddens, H. A. W. M., Maitland-Van der Zee, A. H., Chalmers, J. D., Lucas, J. S. A. & Haarman, E. G., 2024, In: ERJ Open Research. 10, 1, 11 p., 00115-2023.

    Research output: Contribution to journalJournal articleResearchpeer-review

  3. Published

    Automatic analysis of bronchus-artery dimensions to diagnose and monitor airways disease in cystic fibrosis

    Lv, Q., Gallardo-Estrella, L., Andrinopoulou, E., Chen, Y., Charbonnier, J., Sandvik, R. M., Caudri, D., Nielsen, Kim G., de Bruijne, Marleen, Ciet, P. & Tiddens, H., 2024, In: Thorax. p. 13-22

    Research output: Contribution to journalJournal articleResearchpeer-review

  4. Published

    Close monitoring and early intervention: management principles for cystic fibrosis in Denmark

    Qvist, T., Nielsen, B. U., Olesen, H. V., Mathiesen, I. H. M., Faurholt-Jepsen, Daniel, Katzenstein, T. L., Helweg-Larsen, J., Rönsholt, F., Jeppesen, M., Olsen, M. F., Buchvald, F. F., Nielsen, Kim G., Jensen-Fangel, S., Pressler, T. & Skov, M., 2024, In: APMIS. 132, 4, p. 223-235 13 p.

    Research output: Contribution to journalReviewResearchpeer-review

  5. Published

    Long-term effects of high-dose systemic corticosteroids on growth and bone mineral density in patients treated for childhood interstitial lung disease (chILD)

    Ring, A. M., Buchvald, F. F., Main, Katharina Maria, Oturai, P. & Nielsen, Kim G., 2024, In: Pediatric Pulmonology. 59, 4, p. 964-973 10 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  6. Published

    Lung Function in Fontan Patients Over a Ten-Year Period: Is the Fontan Circulation Impairing Lung Development?

    Ravndal, M., Idorn, L., Nielsen, Kim G. & Hjortdal, Vibeke Elisabeth, 2024, In: Pediatric Cardiology. 45, p. 500–512 13 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  7. Accepted/In press

    Surfactant protein D is associated with pulmonary manifestations of chronic graft-versus-host disease following hematopoietic stem cell transplantation

    Krarup, A. M., Kielsen, K., Uhlving, H. H., Steffensen, R., Sørum, Maria Ebbesen, Nielsen, Kim G., Buchvald, F. F., Sorensen, G. L. & Muller, Klaus, 2024, (Accepted/In press) In: Pediatric Pulmonology. 5 p.

    Research output: Contribution to journalLetterResearchpeer-review

  8. 2023
  9. Published

    Multiple breath washout and oscillometry after allogenic HSCT: a scoping review

    Sonneveld, N., Rayment, J. H., Robinson, P. D., Usemann, J. & Nielsen, Kim G., 1 Sep 2023, In: European Respiratory Review. 32, 169, 21 p., 220251.

    Research output: Contribution to journalReviewResearchpeer-review

  10. Published

    Diffuse alveolar haemorrhage in children: an international multicentre study

    Ring, A. M., Schwerk, N., Kiper, N., Aslan, A. T., Aurora, P., Ayats, R., Azevedo, I., Bandeira, T., Carlens, J., Castillo-Corullon, S., Cobanoglu, N., Elnazir, B., Emiralioğlu, N., Eyuboglu, T. S., Fayon, M., Gursoy, T. R., Hogg, C., Kötz, K., Karadag, B., Látalová, V. & 21 others, Krenke, K., Lange, J., Manali, E. D., Osona, B., Papiris, S., Proesmann, M., Reix, P., Roditis, L., Rubak, S., Rumman, N., Snijders, D., Stehling, F., Weiss, L., Yalcın, E., Zirek, F., Bush, A., Clement, A., Griese, M., Buchvald, F. F., Nathan, N. & Nielsen, Kim G., 2023, In: ERJ Open Research. 9, 2, 13 p., 00733-2022.

    Research output: Contribution to journalJournal articleResearchpeer-review

  11. Published

    Exercise capacity in the Danish Fontan population remains stable after ten years of follow-up - is physical activity the key to success?

    Ravndal, M., Idorn, L., Nielsen, A. K. M., Kelly, B., Nielsen, Kim G., Nielsen, D. G. & Hjortdal, Vibeke Elisabeth, 2023, In: International Journal of Cardiology. 387, 7 p., 131137.

    Research output: Contribution to journalJournal articleResearchpeer-review

  12. Published

    High levels of antibodies 6 months after COVID-19 vaccination in children with severe chronic diseases: A prospective longitudinal case series

    Nygaard, Ulrikka, Kirkby, N. S., Dungu, K. H. S., Nielsen, Kim G., Masmas, T., Juul, K., Born, P., Buus, Søren & Stensballe, Lone Graff, 2023, In: Acta Paediatrica. 112, 4, p. 802-804 3 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  13. Published

    Nasal nitric oxide measurement in children for the diagnosis of primary ciliary dyskinesia: European Respiratory Society technical standard

    Beydon, N., Kouis, P., Marthin, J. K., Latzin, P., Colas, M., Davis, S. D., Haarman, E., Harris, A. L., Hogg, C., Kilbride, E., Kuehni, C. E., Marangu, D., Nielsen, Kim G., Pendergrast, C., Robinson, P., Rumman, N., Rutter, M., Walker, W. T., Ferkol, T. & Lucas, J. S., 2023, In: European Respiratory Journal. 61, 4, 18 p., 2202031.

    Research output: Contribution to journalJournal articleResearchpeer-review

  14. Published

    Nationwide lung function monitoring from infancy in newborn-screened children with cystic fibrosis

    Sandvik, R. M., Schmidt, M. N., Voldby, C. M., Buchvald, F. F., Olesen, H. V., Olsen, J., Kragh, M. V., Rubak, S. L. M., Pressler, T., Robinson, P. D., Gustafsson, P. M., Skov, M. & Nielsen, Kim G., 2023, In: ERJ Open Research. 9, 5, 14 p., 00317-2023.

    Research output: Contribution to journalJournal articleResearchpeer-review

  15. Published

    Pulmonary radioaerosol mucociliary clearance assessment: searching for genotype-specific differences and potential as an outcome measure in primary ciliary dyskinesia

    Marthin, J. K., Holgersen, M. G., Nielsen, Kim G. & Mortensen, Jann, 2023, In: ERJ Open Research. 9, 6, 11 p., 00685-2023.

    Research output: Contribution to journalJournal articleResearchpeer-review

  16. Published

    Quantitative99mTc-albumin colloid nasal mucociliary clearance as an outcome in primary ciliary dyskinesia

    Marthin, J. K., Nielsen, Kim G. & Mortensen, Jann, 2023, In: ERJ Open Research. 9, 5, 8 p., 00345-2023.

    Research output: Contribution to journalJournal articleResearchpeer-review

  17. Published

    Towards the international interoperability of clinical research networks for rare diseases: recommendations from the IRDiRC Task Force

    Nabbout, R., Zanello, G., Baker, D., Black, L., Brambilla, I., Buske, O. J., Conklin, L. S., Davies, E. H., Julkowska, D., Kim, Y., Klopstock, T., Nakamura, H., Nielsen, Kim G., Pariser, A. R., Pastor, J. C., Scarpa, M., Smith, M., Taruscio, D. & Groft, S., 2023, In: Orphanet Journal of Rare Diseases. 18, 10 p., 109.

    Research output: Contribution to journalJournal articleResearchpeer-review

  18. Published

    Turning lung clearance index on its head. Reference data for SF6 multiple-breath washout derived ventilation distribution efficiency

    Sandvik, R. M., Lindblad, A., Robinson, P. D., Nielsen, Kim G. & Gustafsson, P., 2023, In: Journal of applied physiology (Bethesda, Md. : 1985). 134, 2, p. 316-327 12 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  19. 2022
  20. Published

    An international survey on nasal nitric oxide measurement practices for the diagnosis of primary ciliary dyskinesia

    Beydon, N., Ferkol, T., Harris, A. L., Colas, M., Davis, S. D., Haarman, E., Hogg, C., Kilbride, E., Kouis, P., Kuehni, C. E., Latzin, P., Marangu, D., Marthin, J., Nielsen, Kim G., Robinson, P., Rumman, N., Rutter, M., Walker, W. & Lucas, J. S., 2022, In: ERJ Open Research. 8, 2, 9 p., 00708-2021.

    Research output: Contribution to journalJournal articleResearchpeer-review

  21. Published

    Chronic airway disease in primary ciliary dyskinesia-spiced with geno-phenotype associations

    Nielsen, Kim G., Holgersen, M. G., Crowley, S. & Marthin, J. K., 2022, In: American Journal of Medical Genetics. Part C: Seminars in Medical Genetics. 190, 1, p. 20-35 16 p.

    Research output: Contribution to journalReviewResearchpeer-review

  22. Published

    Contemporary N2 and SF6 multiple breath washout in infants and toddlers with cystic fibrosis

    Sandvik, R. M., Gustafsson, P. M., Lindblad, A., Buchvald, F., Olesen, H. V., Olsen, J. H., Skov, M., Schmidt, M. N., Thellefsen, M. R., Robinson, P. D., Rubak, S., Pressler, T. & Nielsen, Kim G., 2022, In: Pediatric Pulmonology. 57, 4, p. 945-955

    Research output: Contribution to journalJournal articleResearchpeer-review

  23. Published

    Lung function from school age to adulthood in primary ciliary dyskinesia

    Halbeisen, F. S., Pedersen, E. S. L., Goutaki, M., Spycher, B. D., Amirav, I., Boon, M., Cohen-Cymberknoh, M., Crowley, S., Emiralioglu, N., Haarman, E. G., Karadag, B., Koerner-Rettberg, C., Latzin, P., Loebinger, M. R., Lucas, J. S., Mazurek, H., Morgan, L., Marthin, J., Pohunek, P., Santamaria, F. & 5 others, Schwerk, N., Thouvenin, G., Yiallouros, P., Nielsen, Kim G. & Kuehni, C. E., 2022, In: European Respiratory Journal. 60, 4, 2101918.

    Research output: Contribution to journalJournal articleResearchpeer-review

  24. Published

    National multi-centre study found a low prevalence of severely impaired lung function in children and adolescents

    Lukić, A., Buchvald, F., Agertoft, L., Rubak, S., Skov, M., Perch, Michael & Nielsen, Kim G., 2022, In: Acta Paediatrica, International Journal of Paediatrics. 111, 5, p. 1044-1051 8 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  25. Published

    The disease-specific clinical trial network for primary ciliary dyskinesia: PCD-CTN

    Raidt, J., Maitre, B., Pennekamp, P., Altenburg, J., Anagnostopoulou, P., Armengot, M., Bloemsma, L. D., Boon, M., Borrelli, M., Brinkmann, F., Carr, S. B., Carroll, M. P., Castillo-Corullón, S., Coste, A., Cutrera, R., Dehlink, E., Destouches, D. M. S., Di Cicco, M. E., Dixon, L., Emiralioglu, N. & 31 others, Eralp, E. E., Haarman, E. G., Hogg, C., Karadag, B., Kobbernagel, H. E., Lorent, N., Mall, M. A., Marthin, J. K., Martinu, V., Narayanan, M., Ozcelik, U., Peckham, D., Pifferi, M., Pohunek, P., Polverino, E., Range, S., Ringshausen, F. C., Robson, E., Roehmel, J., Rovira-Amigo, S., Santamaria, F., Schlegtendal, A., Szépfalusi, Z., Tempels, P., Thouvenin, G., Ullmann, N., Walker, W. T., Wetzke, M., Yiallouros, P., Omran, H. & Nielsen, Kim G., 2022, In: ERJ Open Research. 8, 3, 00139-2022.

    Research output: Contribution to journalJournal articleResearchpeer-review

  26. Published

    The effect of inhaled hypertonic saline on lung structure in children aged 3–6 years with cystic fibrosis (SHIP-CT): a multicentre, randomised, double-blind, controlled trial

    Tiddens, H. A. W. M., Chen, Y., Andrinopoulou, E. R., Davis, S. D., Rosenfeld, M., Ratjen, F., Kronmal, R. A., Hinckley Stukovsky, K. D., Dasiewicz, A., Stick, S. M., Anthony, M. M., Au, J., Belessis, Y., Bonte, M., Cheney, J., Clem, C., Clements, B., Cooper, P., Davis, S. D., Davis, M. & 31 others, de Boeck, K., de Marchis, M., De Wachter, E., Delaisi, B., Delaup, V., DeRicco, A., Foti, A., Gan, R., Garriga, L., Gartner, S., Genatossio, A., Grogan, S., Hilton, J., Hoppe, J. E., Janssens, H. M., Jensen, R., Johnson, R., Kemner-van de Corput, M. P. C., Klein, B., Kronmal, R. A., Lucca, F., Lucidi, V., Montemitro, E., Nahidi, L., Nielsen, Kim G., Pearce, K., Pittman, J. E., Powers, M., Sandvik, R. M., Smith, J. & SHIP-CT Study Group, S. S. G., 2022, In: The Lancet Respiratory Medicine. 10, 7, p. 669-678 10 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  27. 2021
  28. Published

    Autologous fibrin sealant co-delivered with antibiotics is a robust method for topical antibiotic treatment after sinus surgery

    Aanæs, Kasper, Nielsen, Kim G., Arndal, E., von Buchwald, Christian, Pressler, T. & Høiby, Niels, 1 Feb 2021, In: Acta Oto-Laryngologica. 141, 2, p. 181-186 6 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  29. Published

    A retrospective review of Achromobacter species and antibiotic treatments in patients with primary ciliary dyskinesia

    Holgersen, M. G., Marthin, J. K., Johansen, Helle Krogh & Nielsen, Kim G., 2021, In: Chronic Respiratory Disease. 18

    Research output: Contribution to journalJournal articleResearchpeer-review

  30. Published

    Characteristics and impact of exercise-induced laryngeal obstruction: an international perspective

    Walsted, E. S., Famokunwa, B., Andersen, L., Rubak, S. L., Buchvald, F., Pedersen, Lars Kliesch, Dodd, J., Backer, Vibeke, Nielsen, Kim G., Getzin, A. & Hull, J. H., 2021, In: ERJ Open Research. 7, 2

    Research output: Contribution to journalJournal articleResearchpeer-review

  31. Published

    Current and future treatments in primary ciliary dyskinesia

    Paff, T., Omran, H., Nielsen, Kim G. & Haarman, E. G., 2021, In: International Journal of Molecular Sciences. 22, 18, 9834.

    Research output: Contribution to journalReviewResearchpeer-review

  32. Published

    Improved agreement between N2and SF6multiple-breath washout in healthy infants and toddlers with improved EXHALYZER D sensor performance

    Sandvik, R. M., Gustafsson, P. M., Lindblad, A., Robinson, P. D. & Nielsen, Kim G., 2021, In: Journal of Applied Physiology. 131, 1, p. 107-118 12 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  33. Published

    International BEAT-PCD consensus statement for infection prevention and control for primary ciliary dyskinesia in collaboration with ERN-LUNG PCD Core Network and patient representatives

    Marthin, J. K., Lucas, J. S., Boon, M., Casaulta, C., Crowley, S., Destouches, D. M. S., Eber, E., Escribano, A., Haarman, E., Hogg, C., Maitre, B., Marsh, G., Martinu, V., Moreno-Galdó, A., Mussaffi, H., Omran, H., Pohunek, P., Rindlisbacher, B., Robinson, P., Snijders, D. & 4 others, Walker, W. T., Yiallouros, P., Johansen, Helle Krogh & Nielsen, Kim G., 2021, In: ERJ Open Research. 7, 3, 14 p., 00301-2021.

    Research output: Contribution to journalJournal articleResearchpeer-review

  34. Published

    Prospective longitudinal association between repeated multiple breath washout measurements and computed tomography scores in children with cystic fibrosis

    Sandvik, R. M., Kongstad, Thomas, Green, K., Voldby, C., Buchvald, F., Skov, M., Pressler, T. & Nielsen, Kim G., 2021, In: Journal of Cystic Fibrosis. 20, 4, p. 632-640 9 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  35. Published

    Withdrawal of dornase alfa increases ventilation inhomogeneity in children with cystic fibrosis

    Voldby, C., Green, K., Philipsen, L., Sandvik, R. M., Skov, M., Buchvald, F., Pressler, T. & Nielsen, Kim G., 2021, In: Journal of Cystic Fibrosis. 20, 6, p. 949-956

    Research output: Contribution to journalJournal articleResearchpeer-review

  36. 2020
  37. Published

    SPEF2- and HYDIN-Mutant Cilia Lack the Central Pair-associated Protein SPEF2, Aiding Primary Ciliary Dyskinesia Diagnostics

    Cindrić, S., Dougherty, G. W., Olbrich, H., Hjeij, R., Loges, N. T., Amirav, I., Philipsen, M. C., Marthin, J. K., Nielsen, Kim G., Sutharsan, S., Raidt, J., Werner, C., Pennekamp, P., Dworniczak, B. & Omran, H., Mar 2020, In: American Journal of Respiratory Cell and Molecular Biology. 62, 3, p. 382-396 15 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  38. Published

    The Controversies and Difficulties of Diagnosing Primary Ciliary Dyskinesia

    Shoemark, A., Rubbo, B., Haarman, E., Hirst, R. A., Hogg, C., Jackson, C. L., Nielsen, Kim G., Papon, J., Robinson, P., Walker, W. T. & Lucas, J. S., 1 Jan 2020, In: American Journal of Respiratory and Critical Care Medicine. 201, 1, p. 120-122 3 p.

    Research output: Contribution to journalComment/debateResearchpeer-review

  39. Published

    Access to medicines for rare diseases: beating the drum for primary ciliary dyskinesia

    Crowley, S., Azevedo, I., Boon, M., Bush, A., Eber, E., Haarman, E., Karadag, B., Kötz, K., Leigh, M., Moreno-Galdó, A., Mussaffi, H., Nielsen, K. G., Omran, H., Papon, J-F., Pohunek, P., Priftis, K., Rindlisbacher, B., Santamaria, F., Valiulis, A., Witt, M. & 4 others, Yiallouros, P., Zivkovic, Z., Kuehni, C. E. & Lucas, J. S., 2020, In: ERJ Open Research. 6, 3, 5 p., 00377-2020.

    Research output: Contribution to journalEditorialResearch

  40. Published

    Efficacy and safety of azithromycin maintenance therapy in primary ciliary dyskinesia (BESTCILIA): a multicentre, double-blind, randomised, placebo-controlled phase 3 trial

    Kobbernagel, H. E., Buchvald, F. F., Haarman, E. G., Casaulta, C., Collins, S. A., Hogg, C., Kuehni, C. E., Lucas, J. S., Moser, Claus Ernst, Quittner, A. L., Raidt, J., Rosthøj, Susanne, Sorensen, A. L., Thomsen, K., Werner, C., Omran, H. & Nielsen, Kim G., 2020, In: The Lancet Respiratory Medicine. 8, 5, p. 493-505 13 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  41. Published

    Lung clearance index-triggered intervention in children with cystic fibrosis – A randomised pilot study

    Voldby, C., Green, K., Kongstad, T., Ring, A. M., Sandvik, R. M., Skov, M., Buchvald, F., Pressler, T. & Nielsen, Kim G., 2020, In: Journal of Cystic Fibrosis. 19, 6, p. 934-941 8 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  42. Published

    Lung compartment analysis assessed from N2 multiple-breath washout in children with cystic fibrosis

    Skov, L., Green, K., Stanojevic, S., Jensen, R., Buchvald, F., Ratjen, F. & Nielsen, Kim G., 2020, In: Pediatric Pulmonology. 55, 7, p. 1671-1680 10 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  43. Published

    Motile ciliopathies

    Wallmeier, J., Nielsen, Kim G., Kuehni, C. E., Lucas, J. S., Leigh, M. W., Zariwala, M. A. & Omran, H., 2020, In: Nature Reviews Disease Primers. 6, 77.

    Research output: Contribution to journalJournal articleResearchpeer-review

  44. Published

    Primary ciliary dyskinesia patients have the same P. aeruginosa clone in sinuses and lungs

    Arndal, E., Johansen, Helle Krogh, Haagensen, J. A. J., Bartell, J. A., Marvig, R. L., Alanin, M., Aanæs, Kasper, Høiby, Niels, Nielsen, Kim G., Backer, Vibeke & von Buchwald, Christian, 2020, In: The European Respiratory Journal. 55, 1, 4 p., 1901472.

    Research output: Contribution to journalLetterResearchpeer-review

  45. Published

    Proceedings of the 4th BEAT-PCD Conference and 5th PCD Training School

    Gardner, L. E., Horton, K. L., Shoemark, A., Lucas, J. S., Nielsen, K. G., Kobbernagel, H., Rubbo, B., Hirst, R. A., Kouis, P., Ullmann, N., Reula, A., Rumman, N., Mitchison, H. M., Pinto, A., Richardson, C., Schmidt, A., Thompson, J., Gaupmann, R., Dabrowski, M., Mill, P. & 5 others, Carr, S. B., Norris, D. P., Kuehni, C. E., Goutaki, M. & Hogg, C., 2020, In: BMC Proceedings. 14, Suppl 8, 17 p., 7.

    Research output: Contribution to journalComment/debateResearch

  46. Published

    Registries and collaborative studies for primary ciliary dyskinesia in Europe

    Ardura-Garcia, C., Goutaki, M., Carr, S. B., Crowley, S., Halbeisen, F. S., Nielsen, Kim G., Pennekamp, P., Raidt, J., Thouvenin, G., Yiallouros, P. K., Omran, H. & Kuehni, C. E., 2020, In: ERJ Open Research. 6, 2, 15 p., 00005-2020.

    Research output: Contribution to journalReviewResearchpeer-review

  47. Published

    Standardised clinical data from patients with primary ciliary dyskinesia: FOLLOW-PCD

    Goutaki, M., Papon, J-F., Boon, M., Casaulta, C., Eber, E., Escudier, E., Halbeisen, F. S., Harris, A., Hogg, C., Honore, I., Jung, A., Karadag, B., Koerner-Rettberg, C., Legendre, M., Maitre, B., Nielsen, K. G., Rubbo, B., Rumman, N., Schofield, L., Shoemark, A. & 4 others, Thouvenin, G., Willkins, H., Lucas, J. S. & Kuehni, C. E., 2020, In: ERJ Open Research. 6, 1, 10 p., 00237-2019.

    Research output: Contribution to journalJournal articleResearchpeer-review

  48. 2019
  49. Published

    Prevalence and course of disease after lung resection in primary ciliary dyskinesia: A cohort & nested case-control study

    Kouis, P., Goutaki, M., Halbeisen, F. S., Gioti, I., Middleton, N., Amirav, I., Barbato, A., Behan, L., Boon, M., Emiralioglu, N., Haarman, E. G., Karadag, B., Koerner-Rettberg, C., Lazor, R., Loebinger, M. R., Maitre, B., Mazurek, H., Morgan, L., Nielsen, K. G., Omran, H. & 9 others, Özçelik, U., Price, M., Pogorzelski, A., Snijders, D., Thouvenin, G., Werner, C., Zivkovic, Z., Kuehni, C. E. & Yiallouros, P. K., Sep 2019, In: Respiratory research. 20, 12 p., 212.

    Research output: Contribution to journalJournal articleResearchpeer-review

  50. Published

    Pulmonary exacerbations in patients with primary ciliary dyskinesia: an expert consensus definition for use in clinical trials

    Lucas, J. S., Gahleitner, F., Amorim, A., Boon, M., Brown, P., Constant, C., Cook, S., Crowley, S., Destouches, D. M. S., Eber, E., Mussaffi, H., Haarman, E., Harris, A., Koerner-Rettberg, C., Kuehni, C. E., Latzin, P., Loebinger, M. R., Lorent, N., Maitre, B., Moreno-Galdó, A. & 10 others, Nielsen, Kim G., Özçelik, U., Philipsen, L. K. D., Pohunek, P., Polverino, E., Rademacher, J., Robinson, P., Snijders, D., Yiallouros, P. & Carr, S. B., Feb 2019, In: ERJ Open Research. 5, 1, 8 p., 00147-2018.

    Research output: Contribution to journalJournal articleResearchpeer-review

  51. Published

    Late Breaking Abstract - Efficacy and safety of azithromycin maintenance therapy in primary ciliary dyskinesia - The BESTCILIA randomized placebo-controlled trial

    Kobbernagel, H., Buchvald, F. F., Haarman, E. G., Casaulta, C., Collins, S. A., Hogg, C., Kuehni, C. E., Lucas, J. S., Omran, H., Quittner, A. L., Werner, C., Rosthøj, Susanne, Sorensen, A. L. & Nielsen, Kim G., 2019, In: European Respiratory Journal. 54, Supplement 63, RCT5102.

    Research output: Contribution to journalConference abstract in journalResearchpeer-review

  52. Published

    Long-Term Lung Function and Exercise Capacity in Postinfectious chILD

    Sisman, Y., Buchvald, F. F., Ring, A. M., Wassilew, K. & Nielsen, Kim G., 2019, In: Pediatric Allergy, Immunology, and Pulmonology. 32, 1, p. 4-11 8 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  53. Published

    Lung clearance index for early detection of pulmonary complications after allo-HSCT in children

    Uhlving, H. H., Skov, L., Buchvald, F., Heilmann, C., Grell, Kathrine, Ifversen, M., Green, K., Muller, Klaus & Nielsen, Kim G., 2019, In: Pediatric Pulmonology. 54, 7, p. 1029-1038 10 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  54. Published

    One-year evolution and variability in multiple-breath washout indices in children and young adults with primary ciliary dyskinesia

    Kobbernagel, H. E., Green, K., Ring, A. M., Buchvald, F. F., Rosthøj, Susanne, Gustafsson, P. M. & Nielsen, Kim G., 2019, In: European Clinical Respiratory Journal. 6, 1, 9 p., 1591841.

    Research output: Contribution to journalJournal articleResearchpeer-review

  55. Published

    Randomization of Left-right Asymmetry and Congenital Heart Defects: The Role of DNAH5 in Humans and Mice

    Nöthe-Menchen, T., Wallmeier, J., Pennekamp, P., Höben, I. M., Olbrich, H., Loges, N. T., Raidt, J., Dougherty, G. W., Hjeij, R., Dworniczak, B., Omran, H., PCD study group, P. S. G., Amirav, I., Biebach, L., Fabricius, D., Nielsen, Kim G., Tebbe, J., Werner, C. & Zariwala, M. A., 2019, In: Circulation. Genomic and precision medicine. 12, 11, p. 513-525

    Research output: Contribution to journalJournal articleResearchpeer-review

  56. Published

    The impact of mannose‐binding lectin polymorphisms on lung function in primary ciliary dyskinesia

    Videbæk, K., Buchvald, F., Holgersen, M. G., Henriksen, A., Eriksson, Frank, Garred, Peter & Nielsen, Kim G., 2019, In: Pediatric Pulmonology. 54, 8, p. 1182-1189 8 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  57. 2018
  58. Published

    Variability of monthly nitrogen multiple-breath washout during one year in children with cystic fibrosis

    Green, K., Kongstad, T., Skov, M., Buchvald, F., Rosthøj, Susanne, Marott, J. L., Gustafsson, P., Pressler, T. & Nielsen, Kim G., Mar 2018, In: Journal of Cystic Fibrosis. 17, 2, p. 242-248 7 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  59. Published
  60. Published

    Associations of physical activity with childhood asthma, a population study based on the WHO - health behaviour in school-aged children survey

    Lochte, Lene, Petersen, Poul Erik, Nielsen, Kim G., Andersen, A. & Platts-Mills, T. A. E., 2018, In: Asthma Research and Practice. 4, p. 1-8 6.

    Research output: Contribution to journalJournal articleResearchpeer-review

  61. Published

    Can secretory immunoglobulin A in saliva predict a change in lung infection status in patients with cystic fibrosis? A prospective pilot study

    Alanin, M. C., Pressler, T., Aanæs, Kasper, Ekstrøm, Claus Thorn, Skov, M., Johansen, Helle Krogh, Nielsen, Kim G., von Buchwald, Christian & Høiby, Niels, 2018, In: Health Services Research. 1, 8, 5 p., e52.

    Research output: Contribution to journalJournal articleResearchpeer-review

  62. Published

    Fitness and lung function in children with primary ciliary dyskinesia and cystic fibrosis

    Ring, A. M., Buchvald, F. F., Holgersen, M. G., Green, K. & Nielsen, Kim G., 2018, In: Respiratory Medicine. 139, p. 79-85

    Research output: Contribution to journalJournal articleResearchpeer-review

  63. Published

    Induced hypothermia in patients with septic shock and respiratory failure (CASS): a randomised, controlled, open-label trial

    Itenov, T. S., Johansen, M. E., Bestle, M., Thormar, K., Hein, L., Gyldensted, L., Lindhardt, A., Christensen, H., Estrup, S., Pedersen, H. P., Harmon, M., Soni, U. K., Perez-Protto, S., Wesche, N., Skram, U., Petersen, J. A., Mohr, T., Waldau, T., Poulsen, L. M., Strange, D. & 12 others, Juffermans, N. P., Sessler, D. I., Tønnesen, E., Møller, Kirsten, Kristensen, D. K., Cozzi-Lepri, A., Lundgren, Jens, Jensen, J., Cooling and Surviving Septic Shock (CASS) Trial Collaboration, C. A. S. S. S. (. T. C., Hägi-Pedersen, Daniel, Poulsen, Anne & Nielsen, Kim G., 2018, In: The Lancet Respiratory Medicine. 6, 3, p. 183-192

    Research output: Contribution to journalJournal articleResearchpeer-review

  64. Published

    Infant nasal nitric oxide over time: natural evolution and impact of respiratory tract infection

    Marthin, J. K., Philipsen, M. C., Rosthøj, Susanne & Nielsen, Kim G., 2018, In: European Respiratory Journal. 51, 6, 8 p., 1702503.

    Research output: Contribution to journalJournal articleResearchpeer-review

  65. Published

    Initiating transitional care for adolescents with cystic fibrosis at the age of 12 is both feasible and promising

    Skov, M., Teilmann, Grete Katrine, Damgaard, I. N., Nielsen, Kim G., Hertz, P. G., Holgersen, M. G., Presfeldt, M., Dalager, A. M. S., Brask, M. & Boisen, K. A., 2018, In: Acta Paediatrica. 107, 11, p. 1977-1982 6 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  66. Published

    Lung function in patients with primary ciliary dyskinesia: an iPCD Cohort study

    Halbeisen, F. S., Goutaki, M., Spycher, B. D., Amirav, I., Behan, L., Boon, M., Hogg, C., Casaulta, C., Crowley, S., Haarman, E. G., Karadag, B., Koerner-rettberg, C., Loebinger, M. R., Mazurek, H., Morgan, L., Nielsen, K. G., Omran, H., Santamaria, F., Schwerk, N., Thouvenin, G. & 4 others, Yiallouros, P., Lucas, J., Latzin, P. & Kuehni, C. E., 2018, In: European Respiratory Journal. 52, 2, 1801040.

    Research output: Contribution to journalJournal articleResearchpeer-review

  67. Published

    Proceedings of the 2nd BEAT-PCD conference and 3rd PCD training school: Part 1

    Halbeisen, F., Hogg, C., Alanin, M. C., Bukowy-Bieryllo, Z., Dasi, F., Duncan, J., Friend, A., Goutaki, M., Jackson, C., Keenan, V., Harris, A., Hirst, R. A., Latzin, P., Marsh, G., Nielsen, K., Norris, D., Pellicer, D., Reula, A., Rubbo, B., Rumman, N. & 4 others, Shoemark, A., Walker, W. T., Kuehni, C. E. & Lucas, J. S., 2018, In: B M C Proceedings. 12, Suppl. 2, 17 p., 1.

    Research output: Contribution to journalComment/debateResearch

  68. Published

    The accessibility of topical treatment in the paranasal sinuses on operated cystic fibrosis patients assessed by scintigraphy

    Aanæs, Kasper, Alanin, M. C., Nielsen, Kim G., Jørgensen, M. M., von Buchwald, Christian, Høiby, N., Johansen, Helle Krogh, Johannesen, H. H. & Mortensen, Jann, 2018, In: Rhinology. 56, 3, p. 268-273

    Research output: Contribution to journalJournal articleResearchpeer-review

  69. Published

    The effect of time-of-day and chest physiotherapy on multiple breath washout measures in children with clinically stable cystic fibrosis

    Voldby, C., Green, K., Rosthøj, Susanne, Kongstad, T., Philipsen, L., Buchvald, F., Skov, M., Pressler, T., Gustafsson, P. & Nielsen, Kim G., 2018, In: PLoS ONE. 13, 1, 15 p., e0190894.

    Research output: Contribution to journalJournal articleResearchpeer-review

  70. Published

    Ventilation inhomogeneity and NO and CO diffusing capacity in ex-premature school children

    Sørensen, J. K., Buchvald, F., Berg, A. K., Robinson, P. D. & Nielsen, Kim G., 2018, In: Respiratory Medicine. 140, p. 94-100

    Research output: Contribution to journalJournal articleResearchpeer-review

  71. 2017
  72. Published

    Fractional exhaled nitric oxide and multiple breath nitrogen washout in preschool healthy and asthmatic children

    Vilmann, L., Buchvald, F., Green, K. & Nielsen, Kim G., Dec 2017, In: Respiratory Medicine. 133, p. 42-47 6 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  73. Published

    Patient-specific three-dimensional explant spheroids derived from human nasal airway epithelium: a simple methodological approach for ex vivo studies of primary ciliary dyskinesia

    Marthin, J. K., Stevens, E. M., Larsen, Lars Allan, Christensen, Søren Tvorup & Nielsen, Kim G., 23 Mar 2017, In: Cilia. 6, 9 p., 3.

    Research output: Contribution to journalJournal articleResearchpeer-review

  74. Published

    Sinus surgery can improve quality of life, lung infections, and lung function in patients with primary ciliary dyskinesia

    Alanin, M. C., Aanæs, Kasper, Høiby, Niels, Pressler, T., Skov, M., Nielsen, Kim G., Johansen, Helle Krogh & von Buchwald, Christian, Mar 2017, In: International Forum of Allergy Rhinology. 7, 3, p. 240-247

    Research output: Contribution to journalJournal articleResearchpeer-review

  75. Published

    Association between spirometry controlled chest CT scores using computer-animated biofeedback and clinical markers of lung disease in children with cystic fibrosis

    Kongstad, T., Green, K., Buchvald, F., Skov, M., Pressler, T. & Nielsen, Kim G., 2017, In: European Clinical Respiratory Journal. 4, 1, 10 p., 1318027 .

    Research output: Contribution to journalJournal articleResearchpeer-review

  76. Published

    Cardiopulmonary Exercise Testing in Fontan Patients With and Without Isomerism (Heterotaxy) as Compared to Patients With Primary Ciliary Dyskinesia and Subjects With Structurally Normal Hearts

    Loomba, R. S., Danduran, M., Nielsen, Kim G., Ring, A. M., Kovach, J. & Anderson, R. H., 2017, In: Pediatric Cardiology. 38, 2, p. 410-417

    Research output: Contribution to journalJournal articleResearchpeer-review

  77. Published

    Clinical care of children with primary ciliary dyskinesia

    Lucas, J. S., Alanin, M. C., Collins, S., Harris, A., Johansen, Helle Krogh, Nielsen, Kim G., Papon, J. F., Robinson, P. & Walker, W. T., 2017, In: Expert Review of Respiratory Medicine. 11, 10, p. 779-790 12 p.

    Research output: Contribution to journalReviewResearchpeer-review

  78. 2016
  79. Published

    Specific airway resistance in preschool children: why not panting after all?

    Ioan, I., Demoulin-Alexikova, S., Coutier, L., Bonabel, C., Kirkby, J., Nielsen, Kim G., Tomalak, W., Thompson, B., Schweitzer, C., Robinson, P. D. & Marchal, F., Dec 2016, In: European Respiratory Journal. 48, 6, p. 1804-1807 4 p.

    Research output: Contribution to journalComment/debateResearch

  80. Published

    Pulmonary function and fitness years after treatment for hypersensitivity pneumonitis during childhood

    Sisman, Y., Buchvald, F. F., Blyme, A. K., Mortensen, Jann & Nielsen, Kim G., Aug 2016, In: Pediatric Pulmonology. 51, 8, p. 830-837 8 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  81. Abbreviation modalities of nitrogen multiple-breath washout tests in school children with obstructed lung disease

    Green, K., Ejlertsen, J. S., Madsen, A., Buchvald, F. F., Kongstad, T., Kobbernagel, H., Gustafsson, P. M. & Nielsen, Kim G., Jun 2016, In: Pediatric Pulmonology. 51, 6, p. 624-32 9 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  82. Published

    Bacterial evolution in PCD and CF patients follows the same mutational steps

    Sommer, L. M., Alanin, M. C., Marvig, R. L., Nielsen, Kim G., Høiby, Niels, von Buchwald, Christian, Molin, S. & Johansen, Helle Krogh, 2016, In: Scientific Reports. 6, 8 p., 28732.

    Research output: Contribution to journalJournal articleResearchpeer-review

  83. Published

    Childhood asthma and physical activity: a systematic review with meta-analysis and Graphic Appraisal Tool for Epidemiology assessment

    Lochte, Lene, Nielsen, Kim G., Petersen, Poul Erik & Platts-Mills, T. A. E., 2016, In: B M C Pediatrics. 16, 13 p., 50.

    Research output: Contribution to journalJournal articleResearchpeer-review

  84. Published

    Natural Evolution And Impact Of Respiratory Tract Infections In Nasal Nitric Oxide Level During First 2 Years Of Life: A Longitudinal Study

    Marthin, J. K., Philipsen, M. C., Rosthøj, Susanne & Nielsen, Kim G., 2016, In: American Journal of Respiratory and Critical Care Medicine. 193, p. 1-2 2 p., A7203.

    Research output: Contribution to journalConference abstract in journalResearchpeer-review

  85. 2014
  86. Published

    Exhaled breath analysis using electronic nose in cystic fibrosis and primary ciliary dyskinesia patients with chronic pulmonary infections

    Joensen, O., Paff, T., Haarman, E. G., Skovgaard, I. M., Jensen, Peter Østrup, Bjarnsholt, Thomas & Nielsen, Kim G., 2014, In: PLOS ONE. 9, 12, p. 1-15 15 p., e115584.

    Research output: Contribution to journalJournal articleResearchpeer-review

  87. 2013
  88. Published

    Interactive 3D computer model of the human corneolimbal region: crypts, projections and stem cells

    Molvaer, R. K., Andreasen, A., Heegaard, Steffen, Thomsen, J. S., Hjortdal, J., Urbak, S. F. & Nielsen, Kim G., Aug 2013, In: Acta Ophthamologica (Online). 91, 5, p. 457-62 6 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  89. Published

    A cohort study of the Copenhagen CF Centre eradication strategy against Staphylococcus aureus in patients with CF

    Dalbøge, C. S., Pressler, T., Høiby, Niels, Nielsen, Kim G. & Johansen, Helle Krogh, Jan 2013, In: Journal of Cystic Fibrosis. 12, 1, p. 42-8 7 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  90. Published

    Can flow-volume loops be used to diagnose exerciseinduced laryngeal obstructions? A comparison study examining the accuracy and inter-rater agreement of flowvolume loops as a diagnostic tool

    Christensen, P. M., Maltbæk, N., Jørgensen, Inger Merete & Nielsen, Kim G., 2013, In: Primary Care Respiratory Journal. 22, 3, p. 306-311 6 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  91. Published

    Clinical effects of sinus surgery and adjuvant therapy in cystic fibrosis patients - can chronic lung infections be postponed?

    Aanæs, Kasper, Johansen, Helle Krogh, Skov, M., Buchvald, F. F., Hjuler, Thomas, Pressler, T., Høiby, Niels, Nielsen, Kim G. & von Buchwald, Christian, 2013, In: Rhinology. 51, 3, p. 222-230 9 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  92. Published

    Enzyme replacement therapy for alpha-mannosidosis: 12 months follow-up of a single centre, randomised, multiple dose study

    Borgwardt, L. G., Dali, C. I., Fogh, J., Månsson, J., Olsen, K. J., Beck, H. C., Nielsen, K. G., Nielsen, L. H., Olsen, S. O. E., Riise Stensland, H. M. F., Nilssen, O., Wibrand, F., Thuesen, A-M., Pearl, T., Haugsted, U., Saftig, P., Blanz, J., Jones, S., Tylki-Szymanska, A., Guffon-Fouiloux, N. & 2 others, Beck, M. V. & Lund, A. M., 2013, In: Journal of Inherited Metabolic Disease. 36, 6, p. 1015-1024 10 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  93. 2012
  94. Published

    Colonisation and infection of the paranasal sinuses in cystic fibrosis patients is accompanied by a reduced PMN response

    Johansen, Helle Krogh, Aanæs, Kasper, Pressler, T., Nielsen, Kim G., Fisker, J., Skov, M., Høiby, Niels & von Buchwald, Christian, Dec 2012, In: Journal of Cystic Fibrosis. 11, 6, p. 525-531 7 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  95. 2010
  96. Published

    Lung function in patients with primary ciliary dyskinesia: a cross-sectional and 3-decade longitudinal study

    Marthin, J. K., Petersen, N., Skovgaard, Lene Theil & Nielsen, Kim G., 2010, In: American Journal of Respiratory and Critical Care Medicine. 181, 11, p. 1262-1268 7 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  97. 2008
  98. Published

    Immunohistochemical markers for corneal stem cells in the early developing human eye

    Lyngholm, M., Høyer, P. E., Vorum, H., Nielsen, Kim G., Ehlers, N. & Møllgård, Kjeld, 2008, In: Experimental Eye Research. 87, 2, p. 115-21 6 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

ID: 916894