Kim G. Nielsen

Kim G. Nielsen

Clinical Professor

Member of:

  • Paediatrics


  1. 2021
  2. Published

    A retrospective review of Achromobacter species and antibiotic treatments in patients with primary ciliary dyskinesia

    Holgersen, M. G., Marthin, J. K., Johansen, Helle Krogh & Nielsen, Kim G., 2021, In: Chronic Respiratory Disease. 18

    Research output: Contribution to journalJournal articleResearchpeer-review

  3. Published

    International BEAT-PCD consensus statement for infection prevention and control for primary ciliary dyskinesia in collaboration with ERN-LUNG PCD Core Network and patient representatives

    Marthin, J. K., Lucas, J. S., Boon, M., Casaulta, C., Crowley, S., Destouches, D. M. S., Eber, E., Escribano, A., Haarman, E., Hogg, C., Maitre, B., Marsh, G., Martinu, V., Moreno-Galdó, A., Mussaffi, H., Omran, H., Pohunek, P., Rindlisbacher, B., Robinson, P., Snijders, D. & 4 others, Walker, W. T., Yiallouros, P., Johansen, Helle Krogh & Nielsen, Kim G., 2021, In: ERJ Open Research. 7, 3, 14 p., 00301-2021.

    Research output: Contribution to journalJournal articleResearchpeer-review

  4. Published

    Current and future treatments in primary ciliary dyskinesia

    Paff, T., Omran, H., Nielsen, Kim G. & Haarman, E. G., 2021, In: International Journal of Molecular Sciences. 22, 18, 9834.

    Research output: Contribution to journalReviewResearchpeer-review

  5. Published

    Improved agreement between N2and SF6multiple-breath washout in healthy infants and toddlers with improved EXHALYZER D sensor performance

    Sandvik, R. M., Gustafsson, P. M., Lindblad, A., Robinson, P. D. & Nielsen, Kim G., 2021, In: Journal of Applied Physiology. 131, 1, p. 107-118 12 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  6. Published

    Prospective longitudinal association between repeated multiple breath washout measurements and computed tomography scores in children with cystic fibrosis

    Sandvik, R. M., Kongstad, Thomas, Green, K., Voldby, C., Buchvald, F., Skov, M., Pressler, T. & Nielsen, Kim G., 2021, In: Journal of Cystic Fibrosis. 20, 4, p. 632-640 9 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  7. Published

    Withdrawal of dornase alfa increases ventilation inhomogeneity in children with cystic fibrosis

    Voldby, C., Green, K., Philipsen, L., Sandvik, R. M., Skov, M., Buchvald, F., Pressler, T. & Nielsen, Kim G., 2021, In: Journal of Cystic Fibrosis. 20, 6, p. 949-956

    Research output: Contribution to journalJournal articleResearchpeer-review

  8. Published

    Characteristics and impact of exercise-induced laryngeal obstruction: an international perspective

    Walsted, E. S., Famokunwa, B., Andersen, L., Rubak, S. L., Buchvald, F., Pedersen, Lars Kliesch, Dodd, J., Backer, Vibeke, Nielsen, Kim G., Getzin, A. & Hull, J. H., 2021, In: ERJ Open Research. 7, 2

    Research output: Contribution to journalJournal articleResearchpeer-review

  9. 2020
  10. Published

    Registries and collaborative studies for primary ciliary dyskinesia in Europe

    Ardura-Garcia, C., Goutaki, M., Carr, S. B., Crowley, S., Halbeisen, F. S., Nielsen, Kim G., Pennekamp, P., Raidt, J., Thouvenin, G., Yiallouros, P. K., Omran, H. & Kuehni, C. E., 2020, In: ERJ Open Research. 6, 2, 15 p., 00005-2020.

    Research output: Contribution to journalReviewResearchpeer-review

  11. Published

    Primary ciliary dyskinesia patients have the same P. aeruginosa clone in sinuses and lungs

    Arndal, E., Johansen, Helle Krogh, Haagensen, J. A. J., Bartell, J. A., Marvig, R. L., Alanin, M., Aanæs, Kasper, Høiby, Niels, Nielsen, Kim G., Backer, Vibeke & von Buchwald, Christian, 2020, In: The European Respiratory Journal. 55, 1, 4 p., 1901472.

    Research output: Contribution to journalLetterResearchpeer-review

  12. Published

    SPEF2- and HYDIN-Mutant Cilia Lack the Central Pair-associated Protein SPEF2, Aiding Primary Ciliary Dyskinesia Diagnostics

    Cindrić, S., Dougherty, G. W., Olbrich, H., Hjeij, R., Loges, N. T., Amirav, I., Philipsen, M. C., Marthin, J. K., Nielsen, Kim G., Sutharsan, S., Raidt, J., Werner, C., Pennekamp, P., Dworniczak, B. & Omran, H., Mar 2020, In: American Journal of Respiratory Cell and Molecular Biology. 62, 3, p. 382-396 15 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  13. Published

    Access to medicines for rare diseases: beating the drum for primary ciliary dyskinesia

    Crowley, S., Azevedo, I., Boon, M., Bush, A., Eber, E., Haarman, E., Karadag, B., Kötz, K., Leigh, M., Moreno-Galdó, A., Mussaffi, H., Nielsen, K. G., Omran, H., Papon, J-F., Pohunek, P., Priftis, K., Rindlisbacher, B., Santamaria, F., Valiulis, A., Witt, M. & 4 others, Yiallouros, P., Zivkovic, Z., Kuehni, C. E. & Lucas, J. S., 2020, In: ERJ Open Research. 6, 3, 5 p., 00377-2020.

    Research output: Contribution to journalEditorialResearch

  14. Published

    Proceedings of the 4th BEAT-PCD Conference and 5th PCD Training School

    Gardner, L. E., Horton, K. L., Shoemark, A., Lucas, J. S., Nielsen, K. G., Kobbernagel, H., Rubbo, B., Hirst, R. A., Kouis, P., Ullmann, N., Reula, A., Rumman, N., Mitchison, H. M., Pinto, A., Richardson, C., Schmidt, A., Thompson, J., Gaupmann, R., Dabrowski, M., Mill, P. & 5 others, Carr, S. B., Norris, D. P., Kuehni, C. E., Goutaki, M. & Hogg, C., 2020, In: BMC Proceedings. 14, Suppl 8, 17 p., 7.

    Research output: Contribution to journalComment/debateResearch

  15. Published

    Standardised clinical data from patients with primary ciliary dyskinesia: FOLLOW-PCD

    Goutaki, M., Papon, J-F., Boon, M., Casaulta, C., Eber, E., Escudier, E., Halbeisen, F. S., Harris, A., Hogg, C., Honore, I., Jung, A., Karadag, B., Koerner-Rettberg, C., Legendre, M., Maitre, B., Nielsen, K. G., Rubbo, B., Rumman, N., Schofield, L., Shoemark, A. & 4 others, Thouvenin, G., Willkins, H., Lucas, J. S. & Kuehni, C. E., 2020, In: ERJ Open Research. 6, 1, 10 p., 00237-2019.

    Research output: Contribution to journalJournal articleResearchpeer-review

  16. Published

    Efficacy and safety of azithromycin maintenance therapy in primary ciliary dyskinesia (BESTCILIA): a multicentre, double-blind, randomised, placebo-controlled phase 3 trial

    Kobbernagel, H. E., Buchvald, F. F., Haarman, E. G., Casaulta, C., Collins, S. A., Hogg, C., Kuehni, C. E., Lucas, J. S., Moser, Claus Ernst, Quittner, A. L., Raidt, J., Rosthøj, Susanne, Sorensen, A. L., Thomsen, K., Werner, C., Omran, H. & Nielsen, Kim G., 2020, In: The Lancet Respiratory Medicine. 8, 5, p. 493-505 13 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  17. Published

    The Controversies and Difficulties of Diagnosing Primary Ciliary Dyskinesia

    Shoemark, A., Rubbo, B., Haarman, E., Hirst, R. A., Hogg, C., Jackson, C. L., Nielsen, Kim G., Papon, J., Robinson, P., Walker, W. T. & Lucas, J. S., 1 Jan 2020, In: American Journal of Respiratory and Critical Care Medicine. 201, 1, p. 120-122 3 p.

    Research output: Contribution to journalComment/debateResearchpeer-review

  18. Published

    Lung compartment analysis assessed from N2 multiple-breath washout in children with cystic fibrosis

    Skov, L., Green, K., Stanojevic, S., Jensen, R., Buchvald, F., Ratjen, F. & Nielsen, Kim G., 2020, In: Pediatric Pulmonology. 55, 7, p. 1671-1680 10 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  19. Published

    Lung clearance index-triggered intervention in children with cystic fibrosis – A randomised pilot study

    Voldby, C., Green, K., Kongstad, T., Ring, A. M., Sandvik, R. M., Skov, M., Buchvald, F., Pressler, T. & Nielsen, Kim G., 2020, In: Journal of Cystic Fibrosis. 19, 6, p. 934-941 8 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  20. Published

    Motile ciliopathies

    Wallmeier, J., Nielsen, Kim G., Kuehni, C. E., Lucas, J. S., Leigh, M. W., Zariwala, M. A. & Omran, H., 2020, In: Nature Reviews Disease Primers. 6, 77.

    Research output: Contribution to journalJournal articleResearchpeer-review

  21. 2019
  22. Published

    Late Breaking Abstract - Efficacy and safety of azithromycin maintenance therapy in primary ciliary dyskinesia - The BESTCILIA randomized placebo-controlled trial

    Kobbernagel, H., Buchvald, F. F., Haarman, E. G., Casaulta, C., Collins, S. A., Hogg, C., Kuehni, C. E., Lucas, J. S., Omran, H., Quittner, A. L., Werner, C., Rosthøj, Susanne, Sorensen, A. L. & Nielsen, Kim G., 2019, In: European Respiratory Journal. 54, Supplement 63, RCT5102.

    Research output: Contribution to journalConference abstract in journalResearchpeer-review

  23. Published

    One-year evolution and variability in multiple-breath washout indices in children and young adults with primary ciliary dyskinesia

    Kobbernagel, H. E., Green, K., Ring, A. M., Buchvald, F. F., Rosthøj, Susanne, Gustafsson, P. M. & Nielsen, Kim G., 2019, In: European Clinical Respiratory Journal. 6, 1, 9 p., 1591841.

    Research output: Contribution to journalJournal articleResearchpeer-review

  24. Published

    Prevalence and course of disease after lung resection in primary ciliary dyskinesia: A cohort & nested case-control study

    Kouis, P., Goutaki, M., Halbeisen, F. S., Gioti, I., Middleton, N., Amirav, I., Barbato, A., Behan, L., Boon, M., Emiralioglu, N., Haarman, E. G., Karadag, B., Koerner-Rettberg, C., Lazor, R., Loebinger, M. R., Maitre, B., Mazurek, H., Morgan, L., Nielsen, K. G., Omran, H. & 9 others, Özçelik, U., Price, M., Pogorzelski, A., Snijders, D., Thouvenin, G., Werner, C., Zivkovic, Z., Kuehni, C. E. & Yiallouros, P. K., Sep 2019, In: Respiratory research. 20, 12 p., 212.

    Research output: Contribution to journalJournal articleResearchpeer-review

  25. Published

    Pulmonary exacerbations in patients with primary ciliary dyskinesia: an expert consensus definition for use in clinical trials

    Lucas, J. S., Gahleitner, F., Amorim, A., Boon, M., Brown, P., Constant, C., Cook, S., Crowley, S., Destouches, D. M. S., Eber, E., Mussaffi, H., Haarman, E., Harris, A., Koerner-Rettberg, C., Kuehni, C. E., Latzin, P., Loebinger, M. R., Lorent, N., Maitre, B., Moreno-Galdó, A. & 10 others, Nielsen, Kim G., Özçelik, U., Philipsen, L. K. D., Pohunek, P., Polverino, E., Rademacher, J., Robinson, P., Snijders, D., Yiallouros, P. & Carr, S. B., Feb 2019, In: ERJ Open Research. 5, 1, 8 p., 00147-2018.

    Research output: Contribution to journalJournal articleResearchpeer-review

  26. Published

    Randomization of Left-right Asymmetry and Congenital Heart Defects: The Role of DNAH5 in Humans and Mice

    Nöthe-Menchen, T., Wallmeier, J., Pennekamp, P., Höben, I. M., Olbrich, H., Loges, N. T., Raidt, J., Dougherty, G. W., Hjeij, R., Dworniczak, B., Omran, H., PCD study group, P. S. G., Amirav, I., Biebach, L., Fabricius, D., Nielsen, Kim G., Tebbe, J., Werner, C. & Zariwala, M. A., 2019, In: Circulation. Genomic and precision medicine. 12, 11, p. 513-525

    Research output: Contribution to journalJournal articleResearchpeer-review

  27. Published

    Long-Term Lung Function and Exercise Capacity in Postinfectious chILD

    Sisman, Y., Buchvald, F. F., Ring, A. M., Wassilew, K. & Nielsen, Kim G., 2019, In: Pediatric Allergy, Immunology, and Pulmonology. 32, 1, p. 4-11 8 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  28. Published

    Lung clearance index for early detection of pulmonary complications after allo-HSCT in children

    Uhlving, H. H., Skov, L., Buchvald, F., Heilmann, C., Grell, Kathrine, Ifversen, M., Green, K., Muller, Klaus & Nielsen, Kim G., 2019, In: Pediatric Pulmonology. 54, 7, p. 1029-1038 10 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

ID: 916894